A CASE OF LYMPHANGIOLEIOMYOMATOSIS WITH MULTIPLE ANGIOMYOLIPOMAS IN THE KIDNEYS: A CASE REPORT

CK, How SH, Azlin S, Pang YK and Liam (0018) A CASE OF LYMPHANGIOLEIOMYOMATOSIS WITH MULTIPLE ANGIOMYOLIPOMAS IN THE KIDNEYS: A CASE REPORT. Journal of Health and Translational Medicine.

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Abstract

Lymphangioleiomyomatosis (LAM) is a rare disease. The reported prevalence is around one per million in the West but the exact prevalence in Asia is unknown. It affects primarily young women of reproductive age, with a mean age of onset at 34 years. The disease is characterised by an abnormal proliferation of smooth muscle-like cells that grow over a course of time to obstruct airways, lymphatic and blood vessels. We report a case of LAM in a young woman who presented with a spontaneous pneumothorax. Computed tomography scan of the thorax and abdomen showed homogenous thin-walled cystic lesions with normal intervening lung parenchyma and multiple lesions in her kidneys with Hounsfield units similar to that of fat. (JUMMEC 2006; 9(2): 35-38)

Item Type: Article
Uncontrolled Keywords: Lymphangioleiomyomatosis, renal angiomyolipoma, spontaneous pneumothorax, cystic lesions of lungs
Depositing User: MR. ADNAN YAHYA
Date Deposited: 12 Oct 0018
Last Modified: 12 Oct 0018
URI: http://repository.um.edu.my/id/eprint/112005

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